Turkish Neurosurgery 2015 , Vol 25 , Num 5
Moyamoya Disease Associated with Recurrent Right Thalamic Haemorrhage and Hydrocephalous: A Case Report
Rohan SINHA1, Amit Kumar JAIN2, Nitin JAGDHANE1, Parvati NANDY2, Satish Kumar KHANNA3
1Sikkim Manipal Institute of Medical Sciences, Central Referral Hospital, Department of Neurosurgery, Gangtok, Sikkim, India
2Sikkim Manipal Institute of Medical Sciences, Central Referral Hospital, Department of Medicine,Gangtok, Sikkim, India
3Sikkim Manipal Institute of Medical Sciences,Central Referral Hospital, Department of Radiodiagnosis,Gangtok, Sikkim, India
DOI : 10.5137/1019-5149.JTN.11113-14.0 Moyamoya disease, a rare chronic, progressive cerebrovascular disease leads to occlusion of intracranial internal carotid arteries and its proximal branches. We report a case of a 51-year-old female who presented with recurrent thalamic bleed and intraventricular haemorrhage nine years apart in the same territory. The first bleed was managed conservatively and second bleed led to development of hydrocephalus. The acute phase of the hydrocephalus was managed by external ventricular drainage and the final CSF diversion was managed by ventriculoperitoneal shunt. The definitive treatment could not be done to denial of consent from the patient. We present the case to highlight the role CSF diversion as a means of palliative treatment for the Moyamoya disease. Keywords : Moyamoya disease, Adult, Haemorrhage, Hydrocephalus, Ventriculoperitoneal shunt
Corresponding author : Rohan Sřnha, drrohansinha@gmail.com