Turkish Neurosurgery 2013 , Vol 23 , Num 1
Nerve Sheath Myxoma (Neurothekeoma) of Cerebellopontine Angle: Case Report of a Rare Tumor with Brief Review of Literature
Mukul VIJ1, Sushila JAISWAL2, Vinita AGRAWAL2, Awadesh JAISWAL3, Sanjay BEHARI3
1Christian Medical College, Department of Pathology, Vellore, India
2SGPGIMS, Department of Pathology, Lucknow, India
3SGPGIMS, Department of Neurosurgery, Lucknow, India
DOI : 10.5137/1019-5149.JTN.4255-11.1 Nerve sheath myxoma (neurothekeoma) are rare benign nerve sheath tumors, usually arising in the skin of the head and neck region and upper extremities in young females. To the best of author's knowledge only two cases of intracranial neurothekeoma have been published in the English literature. These tumors were located in the parasellar area and in middle cranial fossa. This is the first case report of cerebellopontine angle neurothekeoma and third case report of intracranial neurothekeoma. This patient, a 45-year-old female, presented to us with complaints of right side progressive hearing loss for 12 months and swaying during walking for 8 months. Histologically the tumor had lobular appearance with spindle or stellate cells embedded in abundant myxoid background. The tumor cells were diffusely positive for S100. The patient was symptom free at eight month follow up. Keywords : Nerve sheath myxoma, Neurothekeoma, Intracranial, Cerebellopontine angle
Corresponding author : Mukul Vřj, mukul.vij.path@gmail.com