Turkish Neurosurgery 2013 , Vol 23 , Num 4
Thoracic Vertebral Hemangioma Causing Paraplegia in Klippel-Trenaunay-Weber Syndrome: Case Report
Ozerk OKUTAN1, Timur YILDIRIM1, Serdar ISIK2, Berna GOKCE1, Barıs SAYGILI1, Ethem Bes KONAKLI1
1Ankara Ataturk Education and Research Hospital, Department of Neurosurgery, Ankara, Turkey
2Ordu University, Faculty of Medicine, Department of Neurosurgery, Ordu, Turkey
DOI : 10.5137/1019-5149.JTN.5028-11.1 Vertebral hemangiomas are the most common tumours of the vertebral column. Generally, these tumours are asymptomatic but some patients complain of back pain and develop neurologic symptoms due to extraosseous extension. Vertebral hemangiomas can extend extradurally causing neurological impairment as a result of compression of the spinal cord and nerve roots. Vertebral hemangiomas may be multiple and detectable as a component of the Klippel-Trenaunay-Weber syndrome. Although this syndrome consists of deep venous thrombosis, lymphatic anomalies, cutaneous capillary malformations, and hypertrophy of soft tissue and bone on extremities, its clinical presentation may be very variable. We present a unique case of vertebral hemangioma causing spinal cord compression due to the extradural extension that also had deep venous thrombosis, hematuria, hypophyseal cyst and ventricle asymmetry, diagnosed as the Klippel-Trenaunay-Weber syndrome. Keywords : Thoracic vertebra, Hemangioma, Cord compression, Klippel-Trenaunay-Weber syndrome
Corresponding author : Timur Yıldırım, mdtimur@hotmail.com