Turkish Neurosurgery
2012 , Vol 22 , Num 5
Epidermoid Cyst Inside Anterior Sacral Meningocele in an Adult Patient of Currarino Syndrome Manifesting with Meningitis
Seth G.S. Medical College at K.E.M. Hospital, Department of Neurosurgery, Parel, Mumbai, Indian
DOI :
10.5137/1019-5149.JTN.3985-10.1
The Currarino triad, also known as the “Currarino Syndrome”, is a rare complex of congenital caudal anomalies including three main features;
a sacral bony deformity, anorectal malformations, and a presacral mass. We present an extremely uncommon case of Currarino syndrome in
adulthood presenting with repeated episodes of meningitis. Magnetic resonance imaging of spine was suggestive of caudal regression. Cord
was low lying, conus ending at L3 level with evidence of tethering at that level. A large cyst was noted in the sacral canal extending forwards
in the pelvis through the widened sacral foramina on right side. She was operated through a posterior approach, via sacral laminectomy. Dura
was opened in the midline, large silvery white epidermoid tumor was found completely occupying the anterior sacral meningocele. The case
and relevant literature is discussed.
Keywords :
Anterior sacral meningocele, Currarino syndrome, Epidermoid cyst, Meningitis