Turkish Neurosurgery
2008 , Vol 18 , Num 1
Atypical Teratoid/Rhabdoid Tumors: Imaging Findings of Two Cases and Review of the Literature
1,2Fatih University, Radiology Department, Ankara, Turkey3Hacettepe University, Pathology Department, Ankara, Turkey
429 Mayıs Hospital, Neurosurgery Department, Ankara, Turkey Atypical teratoid/rhabdoid tumor (AT/RT) is a malignant embryonal central nervous system (CNS) tumor, manifesting in children, and composed of rhabdoid cells, with or without fields resembling a classical primitive neuroectodermal tumor (PNET), epithelial tissue and neoplastic mesenchyme. Around 200 cases of CNS AT/RT have been documented in the literature. Although the clinical and pathological findings have been defined in large series previously, and AT/RT has become increasingly recognized, awareness of typical AT/RT is important in making the correct diagnosis of this uncommon but probably underdiagnosed entity. Neuroradiologists rarely mention AT/RT in their differential diagnosis and this paper presents two additional cases in which clinical and pathological findings are combined with neuroradiological presentation. Keywords : Atypical teratoid /rhabdoid tumor, Computerized tomography, Magnetic rezonance imaging