Methods: An 18-year-old female with a red-violet skin lesion on her lower back was determined spina bifida at L5-S1 by x-ray. Magnetic resonance imaging sequences showed a fibrous band arising from a posterior fusion defect at L5-Sl. Light microscopy examination of the specimen were seen islets of meningothelial cells and calcified psammoma bodies spread among the vessels, neuronal structures, and dense collagenous tissue.

Result: We present a case lumbosacral ectopic hamartoma with hypertrichosis and a review of the nomenclature, classification and pathogenesis of this disorder.

Conclusion: Ectopic meningiomas are rare tumors in which etiopathogenesis is not clear. They are usually independent of intracranial meningiomas. These lesions characterize with clinical and pathological diagnostic difficulties. In the literature, these lesions have been given a lot of names like ectopic meningioma, meningial hamartoma, cutenous meningioma. Because this lesion did not consist solely of meningial elements, we suggested that the cases should be more accurately labeled as meningial hamartoma. Keywords : Meningial hamartoma, hypertrichosis, lumbosacral region