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¹Christian Medical College, Department of Pathology, Vellore, India
²SGPGIMS, Department of Pathology, Lucknow, India
³SGPGIMS, Department of Neurosurgery, Lucknow, India DOI : 10.5137/1019-5149.JTN.4255-11.1 Nerve sheath myxoma (neurothekeoma) are rare benign nerve sheath tumors, usually arising in the skin of the head and neck region and upper extremities in young females. To the best of author's knowledge only two cases of intracranial neurothekeoma have been published in the English literature. These tumors were located in the parasellar area and in middle cranial fossa. This is the first case report of cerebellopontine angle neurothekeoma and third case report of intracranial neurothekeoma. This patient, a 45-year-old female, presented to us with complaints of right side progressive hearing loss for 12 months and swaying during walking for 8 months. Histologically the tumor had lobular appearance with spindle or stellate cells embedded in abundant myxoid background. The tumor cells were diffusely positive for S100. The patient was symptom free at eight month follow up. Keywords : Nerve sheath myxoma, Neurothekeoma, Intracranial, Cerebellopontine angle