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¹Nizam's Institute of Medical Sciences, Department of Neurosurgery, Hyderabad, India
²Nizam's Institute of Medical Sciences, Department of Pathology, Hyderabad, India
³NRI Academy of Sciences, Department of Neurosurgery, Guntur, India
⁴Krishna Institute of Medical Sciences, Department of Neurosurgery, Hyderabad, India DOI : 10.5137/1019-5149.JTN.4131-11.1 Ewing's / peripheral primitive neuroectodermal tumor (pPNET) of the cavernous sinus are extremely uncommon. We present clinical, radiological, pathological findings of Ewing's / pPNET involving the cavernous sinus in an eleven-month-old infant presenting with proptosis and 6th nerve palsy. MRI Contrast scans showed a well-defined, homogenously enhancing mass involving the right cavernous sinus location. Histopathology and immunohistochemical features were consistent with Ewing's/pPNET. The patient succumbed to disease in spite of starting chemotherapy. The clinical, radiological and pathological findings of previously reported cases of Ewing's sarcoma / pPNET involving the cavernous sinus are summarized. The histological differential diagnosis of primary intracranial Ewing's sarcoma / pPNET are discussed. Keywords : Ewing's sarcoma, Peripheral primitive neuroectodermal tumor, Cavernous sinus